21 alpha-hydroxlase deficiency: (masculinization, pseudohermaphrodite)
the most common congenital adrenal hyperplasia syndrome
Key feature = Hypotension and dehydration (salt wasting)
11 alpha-hydroxlase deficiency: (Masculinization)
Key feature used to distinguish 11 from 21 = hypertension due to increased mineralcorticoids
17 alpha-hydroxylase deficiency: (fails to mature sexually)
phenotypical female but never matures = no sex hormones = this distinguishes it from 11 because 17 has increased mineralcorticoids and hypertension as well.
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